Acondroplazy - Treatment

Pharmacological Therapy:Growth hormone is now used to enlarge the height acondroplazie patients. The most significant acceleration of growth is observed in the first year of treatment. No studies have been conducted to determine the final height. Starting early at young ages is recommended therapy.
Surgical therapy:The problems discovered in these orthopedic patients are associated with the column. Craniocervicala stenosis, thoracolombar kyphosis, spinal stenosis, angulation deformities of the lower extremities and limb lengthening are problems that can be improved through surgery.Spinal canal stenosis:The practice laminectomii large extend multiple processes until the pedicle and lateral foraminotomii. If there is a herniated disc that is removed rod. Decompression length extends from the lower thoracic spine to the sacrum up to prevent recurrence. If there is instability in the practice fusion.Cifosis thoracolombar:Treatment consists of observation especially for children under outpatient began as spontaneous resolution occurs. If the kyphosis persists after the beginning of walking is used in rtoza toracolombosacrala extension. If the kyphosis persists and widens the age of 5 years after surgery is performed anterior and posterior fusion.Genu varum:Genu varum surgical correction is necessary. You can practice by proximity tibiofibulara epifiziodezis fibular osteotomy.Limb lengthening:This technique is rpromovata in clinics in Europe, but not from the U.S.. With current techniques of osteogenesis is win 30 cm in length. Nerve injuries occur in 35% of cases.Foramen magnum decompression:Foramen collapse is the result of numerous neurological problems early in life. The practice laminectomia C1. Ventriculoperitoneal shunts are indicated for patients with rapid progression to the head enlargement, high intracranial pressure or neurological signs and symptoms.Obstructive sleep apnea:Treatment includes adenotonsilectomie, weight reduction, continuous positive pressure breathing by nasal mask and tracheostomy in extreme cases. These techniques significantly improves sleep apnea.
PrognosisThe mortality rate is high for all ages. In children under 4 years brain death occurs by compression of the base. Persons aged 5-24 years and respiratory problems, central nervous system. In people over 25 years are the most common problems of the cardiovascular system.