Becker muscular dystrophy (DMB) is also a hereditary disease,with the same cormosomul X linked recessive transmission, butwith slower growth and a more benign clinical picture than withDuchenne muscular dystrophy. Protein called dystrophin, the absence in Duchenne's disease, is found in insufficient quantities,and only partially fulfilling the function (to protect the membrane thatwraps the muscle fibers).
Becker muscular dystrophy symptoms are generally lesspronounced than those of Duchenne myopathy. Their onset isvariable, from 2-45 years, mean age of occurrence of symptoms is12 years. Walking ability is preserved after the age of 16 years,and deformation of the spine is less common. Respiratory failure isnot observed before 40 -50 years. Intellectual functions are notaltered. Touching heart is less severe than Duchenne myopathy.
Becker muscular dystrophy is 10 times rarer than Duchennedisease, affecting about three in 10,000 boys. Most people live to50 -60 years, causes of death are the same as with Duchennemyopathy: lung infections and heart failure.
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