Limfangiectazia intestinal (idiopathic hypoproteinemia)

Limfangiectazia intestinal (idiopathic hypoproteinemia) Limfangiectazia bowel disease is characterized by dilation and blockage of lymphatic vessels intestinale.Cauza is abnormal formation of lymphatic vessels. The main symptom is diareea.Diagnosticul is on histological examination of biopsy pieces out of a gut. Lymphatic vessels carry digestive tract digested fats absorbed from the intestine subtire.Anumiti still unknown factors determine the development of these abnormal vessels, the dilation of their lives. Rarely the disease can develop in response to pancreatitis, or constrictive pericarditis. Dilated lymphatic vessels could no longer transport function of lymph chylomicrons and blocking the absorption of proteins in the blood. Pathogenic disease is characterized by hypoproteinemia, edema, and lymphocytopenia, which leading to immune dysfunction, including: hipogammaglobulinemie, and rejection of allogrefa.In anergy may deteriorate further reserves of iron and other trace elements in the body. Mortality is related to diarrhea and massive edema. The disease may be primary - congenital debut at an early age or secondary to other diseases, onset in adulthood. Treatment is symptomatic and includes supplements of Ca, Fe, triglycerides, low consumption of foods rich in fat and protein.
Causes The causes are unknown primary cause intestinal limfangiectazia for the affections of the secondary are: -Abdominal or retroperitoneal carcinoma, lymphoma, Crohn's disease Heart-disease: constrictive pericarditis, congestive heart syndrome -Intestinal tuberculosis, sarcoidosis, chronic pancreatitis, the disease Wipple -Sclerosis, celiac disease, SLE, mesenteric sclerosis, intestinal endometriosis.
Signs and symptoms, diagnosis Shows colon limfangiectazie Opersoana with diarrhea, nausea, vomiting, malabsorption, fatty stools and pain abdominale.De ascites and edema also develops bilateral and unilateral primary limfangiectazia in the secondary. Laboratory diagnosis includes: Hipoproteinemiei-predominant emphasis hypoalbuminemia Α1-trypsin-test demonstrates a lack of seat-protein Abdominal X-ray-imaging tests, double sharp contrast intestinal edema, prominent nodular, mucosal ulceration absent -Computed tomography and magnetic resonance Endoscopy-chorionic-lactescente, lactescenti nodules, prominent submucosal boards xanthomatous deposits -Capsule endoscope -Jejunal-biopsy will reveal the mucosal and submucosal lymphatics dilations.
Treatment Treatment of patients with primary intestinal limfangiectazie includes changes in diet, medication and surgery. Diet changes include: Percentage of fat-reduced foods -Replace the long-chain fat with medium chain -Reducing the amount of salt consumed -Protein diets. May use anti-diarrheal medications, octreotide. Surgery is needed especially in the secondary form of disease.